Table 3.

TNM Staging System for Rhabdomyosarcoma.

Stage	Sites	T	Tumor Size Designation	N	M
I	Orbit Head and neck * Genitourinary † Biliary tract	T1 or T2	a or b	Any N	M0
II	Bladder or prostate Extremity Cranial parameningeal Other ‡	T1 or T2	a	N0 or Nx	M0
III	Bladder or prostate Extremity Cranial parameningeal Other ‡	T1 or T2	a	N1	M0
IV	All	T1 or T2	a or b	N0 or N1	M1

T1, tumor confined to the anatomic site; T2, tumor extension; a, ≤5 cm in diameter; b, >5 cm in diameter; N0, nodes not clinically involved; N1, nodes clinically involved; Nx, clinical status of nodes unknown; M0, no distant metastases; M1, distant metastases present. * Excluding parameningeal sites. † Nonbladder and nonprostate. ‡ Includes trunk, retroperitoneum, etc., excluding biliary tract.