Table 1.

Patient first visit RHS and HFMSE scores, and ages by SMA type, age, and motor function level. N: number of participants, M: number of assessments, IQR: inter-quartile range.

Grouping		N	RHS Median (IQR)	RHS Range	HFMSE Median (IQR)	HFMSE Range	Age Median (IQR)	Age Range
All		177	12 (6–34)	0–69	18 (7–40)	0–66	7.7 (4–10.6)	1–17.5
SMA Type	2	110	7 (4–11)	0–27	9 (4–18)	0–39	6 (3–9.6)	1–17.5
	3a	58	40 (25–48)	7–67	47 (35–51)	7–63	8.8 (5.3–11.5)	2.7–15.7
	3b	9	59 (49–64)	31–69	60 (53–63)	36–66	13.3 (9.4–15.2)	4.2–17.1
Age Group	<5	60	10 (6–23)	3–52	16 (9–34)	3–53	3.2 (2.2–4)	1–4.9
	5–7	33	15 (7–46)	3–67	22 (10–49)	3–63	6.3 (5.5–7.3)	5–7.9
	8–13	64	16 (5–38)	0–65	21 (6–44)	0–63	9.8 (9.1–11.8)	8–13.9
	14–18	20	6 (3–27)	0–69	7 (3–38)	0–66	14.9 (14.6–16.1)	14.2–17.5
WHO-derived Functional Group	Non–Sitter	22	2 (1–4)	0–8	2 (0–4)	0–12	10.3 (6.4–12.6)	1–16.5
	Sitter	98	8 (6–15)	2–26	12 (7–20)	2–40	5.8 (3.3–9.6)	1.2–17.5
	Transitional Group	11	26 (25–29)	18–59	36 (34–38)	24–61	8.7 (6.3–13.1)	2.8–17.1
	Walker	46	46 (41–58)	27–69	49 (47–58)	35–66	8.1 (4.8–10.1)	2.7–15.2
Ambulation	Non– Ambulant	131	8 (4–15)	0–59	11 (5–21)	0–61	7.6 (3.8–10.9)	1–17.5
Gender	Male	94	10 (5–24)	0–69	14 (7–34)	0–66	7.9 (4.5–11.1)	1–17.5
	Female	83	15 (6–40)	0–67	21 (9–45)	0–63	7.3 (3.6–9.9)	1.2–16.6
Spinal Surgery	Yes	23	5 (2–10)	0–59	6 (2–13)	0–61	13.5 (10.2–14.9)	2.2–17.5
	No	126	14 (6–36)	0–69	20 (9–41)	0–66	6.3 (3.6–9.5)	1–15.7
RHS Total Score Group	Q1	36	3 (2–4)	0–4	3 (1–4)	0–8	9.8 (4.9–13.8)	1.5–16.6
	Q2	38	6 (6–7)	5–9	9 (7–11)	4–16	6.1 (2.5–9.6)	1–17.5
	Q3	38	14 (10–16)	10–18	19 (15–23)	11–29	5.1 (3.7–8.6)	1.5–15.7
	Q4	34	28 (25–39)	20–42	38 (34–46)	27–49	9.3 (4.6–10.9)	2.2–16.3
	Q5	31	56 (46–64)	43–69	56 (50–62)	36–66	7.9 (5.5–10.1)	3.3–17.1