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. 2023 Jan 30;31(1):19–28. doi: 10.5606/tgkdc.dergisi.2023.23396

Table 1. Demographic, clinical, and imaging characteristics of ACAPA patients.

Patient no Sex/age
(months/years)
Symptoms Electrocardiography Echocardiography
1 M/8 years Chest pain ST depression in V6 EF: 70%,
LVEDd Z score: 0.35
RCA/AA >1.4,
ICC: +, MR: No,
PMH: -, RDF+
2 F/9.5 years Murmur ALMI EF: 67%,
LVEDd Z score: 1.7
RCA/AA >1.4,
ICC: +, PMH: -
MR: moderate, RDF: +
3t M/13 years Fatigue T negativity in aVL,
V1-V3
Left anterior hemiblock
EF: 66%,
LVEDd Z score: 2.7
ICC: +, PMH: - MR: Severe, RDF: +
4 F/5 months Respiratory distress ALMI EF: 54%,
LVEDd Z score: 7.3
MR: Mild, PMH: +, ICC: +
5* F/5 years No symptoms
(during diagnosis; VSD, follow-up)
Normal EF: 75%
LVEDd Z score: -0.6
LCA/AA >1.3, ICC: +, VSD
6 F/3 months Respiratory distress, diaphoresis, failure to thrive ALMI EF: 40%
LVEDd Z score: 4.2
MR: Severe, ICC: +
PMH: +, RDF: +, RCA/AA >1.4
7 F/6 months Respiratory distress, decreased oral intake, diaphoresis, failure to thrive ALMI EF: 56%
LVDDd Z score: 1.1
MR: Severe, ICC: +, PMH: +
8 F/7 months Shortness of breath, diaphoresis, failure to thrive ALMI EF: 38%
LVEDd Z score: 4.5
PMH: +, MR:severe, RDF
9* M/5.5 years No symptoms
(during diagnosis ASD follow-up)
Incomplete RBBB, T negativity in V1-4 EF: 79%
LVEDd Z score: -0.5 ICC: +, RDF: +, ASD
10 M/2.5 years Respiratory distress, ALMI EF: 60%,
LVEDd Z score: 3.3
MR: Mild
RCA/AA >1.4, PMH: +, ICC: +
11 F/9 months Respiratory distress, diaphoresis, failure to thrive ALMI EF: 64%
LVEDd Z score: 2.8 MR: Moderate, PMH: + ICC: +, RDF: +
RCA/AA >1.4
12 F/3 months Respiratory distress, diaphoresis, failure to thrive ALMI EF: 44%
LVEDd Z score: 5
MR: Moderate, PMH: +
ICC: -, RDF: +
RCA/AA >1.4
13 F/15 months Murmur ALMI EF: 64%
LVEDd Z score: 3.3
MR: Mild, ICC: +
RCA/AA >1.4, PMH: -
14 M/2 years Palpitation ALMI EF: 59%
LVDD Z score: 5.3
MR: Moderate, PMH: +
ICC: +, RCA/AA >1.4
ACAPA: Anomalous origin of coronary artery from the pulmonary artery; EF: Ejection fraction; LVEDd: Left Ventricular End Diastolic Diameter; RCA: Right coronary artery; AA: Aorta artery; ICC: Intercoronary septal collaterals; MR: Mitral regurgitation; PMH: Papillary muscle hyperechogenicity; RDF: Reverse Doppler flow; ALMI: Anterolateral myocardial infarction; LCA: Left coronary artery; VSD: Ventricular septal defect; ASD: Atrial septal defect; RBBB: Right bundle branch block; ARCAPA: Anomalous right coronary artery origin from the pulmonary artery; † This patient had mitral valve surgery at the age of 3 years; * ARCAPA patients.