Table 1. Demographic, clinical, and imaging characteristics of ACAPA patients.
Patient no | Sex/age (months/years) |
Symptoms | Electrocardiography | Echocardiography |
1 | M/8 years | Chest pain | ST depression in V6 | EF: 70%, LVEDd Z score: 0.35 RCA/AA >1.4, ICC: +, MR: No, PMH: -, RDF+ |
2 | F/9.5 years | Murmur | ALMI | EF: 67%, LVEDd Z score: 1.7 RCA/AA >1.4, ICC: +, PMH: - MR: moderate, RDF: + |
3t | M/13 years | Fatigue | T negativity in aVL, V1-V3 Left anterior hemiblock |
EF: 66%, LVEDd Z score: 2.7 ICC: +, PMH: - MR: Severe, RDF: + |
4 | F/5 months | Respiratory distress | ALMI | EF: 54%, LVEDd Z score: 7.3 MR: Mild, PMH: +, ICC: + |
5* | F/5 years | No symptoms (during diagnosis; VSD, follow-up) |
Normal | EF: 75% LVEDd Z score: -0.6 LCA/AA >1.3, ICC: +, VSD |
6 | F/3 months | Respiratory distress, diaphoresis, failure to thrive | ALMI | EF: 40% LVEDd Z score: 4.2 MR: Severe, ICC: + PMH: +, RDF: +, RCA/AA >1.4 |
7 | F/6 months | Respiratory distress, decreased oral intake, diaphoresis, failure to thrive | ALMI | EF: 56% LVDDd Z score: 1.1 MR: Severe, ICC: +, PMH: + |
8 | F/7 months | Shortness of breath, diaphoresis, failure to thrive | ALMI | EF: 38% LVEDd Z score: 4.5 PMH: +, MR:severe, RDF |
9* | M/5.5 years | No symptoms (during diagnosis ASD follow-up) |
Incomplete RBBB, T negativity in V1-4 | EF: 79% LVEDd Z score: -0.5 ICC: +, RDF: +, ASD |
10 | M/2.5 years | Respiratory distress, | ALMI | EF: 60%, LVEDd Z score: 3.3 MR: Mild RCA/AA >1.4, PMH: +, ICC: + |
11 | F/9 months | Respiratory distress, diaphoresis, failure to thrive | ALMI | EF: 64% LVEDd Z score: 2.8 MR: Moderate, PMH: + ICC: +, RDF: + RCA/AA >1.4 |
12 | F/3 months | Respiratory distress, diaphoresis, failure to thrive | ALMI | EF: 44% LVEDd Z score: 5 MR: Moderate, PMH: + ICC: -, RDF: + RCA/AA >1.4 |
13 | F/15 months | Murmur | ALMI | EF: 64% LVEDd Z score: 3.3 MR: Mild, ICC: + RCA/AA >1.4, PMH: - |
14 | M/2 years | Palpitation | ALMI | EF: 59% LVDD Z score: 5.3 MR: Moderate, PMH: + ICC: +, RCA/AA >1.4 |
ACAPA: Anomalous origin of coronary artery from the pulmonary artery; EF: Ejection fraction; LVEDd: Left Ventricular End Diastolic Diameter; RCA: Right coronary artery; AA: Aorta artery; ICC: Intercoronary septal collaterals; MR: Mitral regurgitation; PMH: Papillary muscle hyperechogenicity; RDF: Reverse Doppler flow; ALMI: Anterolateral myocardial infarction; LCA: Left coronary artery; VSD: Ventricular septal defect; ASD: Atrial septal defect; RBBB: Right bundle branch block; ARCAPA: Anomalous right coronary artery origin from the pulmonary artery; † This patient had mitral valve surgery at the age of 3 years; * ARCAPA patients. |