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. Author manuscript; available in PMC: 2024 Mar 27.
Published before final editing as: Clin Exp Ophthalmol. 2022 Sep 27:10.1111/ceo.14175. doi: 10.1111/ceo.14175

Table 1:

Selected Uveitic Diseases

Anatomic class Infectious Systemic Disease Associated Eye-limited
Anterior Cytomegalovirus anterior uveitis Juvenile idiopathic arthritis-associated anterior uveitis Fuchs uveitis syndrome
Herpes simplex virus anterior uveitis Spondyloarthritis/HLA-B27-associated anterior uveitis Undifferentiated anterior uveitis
Varicella zoster virus anterior uveitis Tubulointerstitial nephritis with uveitis
Syphilitic anterior uveitis Sarcoidosis-associated anterior uveitis
Intermediate Syphilitic intermediate uveitis Multiple sclerosis-associated intermediate uveitis Pars planitis
Sarcoidosis-associated intermediate uveitis Intermediate uveitis, non-pars planitis type (undifferentiated intermediate uveitis)
Posterior Acute retinal necrosis Sarcoidosis-associated panuveitis Acute posterior multifocal placoid pigment epitheliopathy
Cytomegalovirus retinitis Birdshot chorioretinitis
Syphilitic posterior uveitis Multiple evanescent white dot syndrome
Toxoplasmic retinitis Multifocal choroiditis with panuveitis
Tuberculous posterior uveitis Punctate inner choroiditis
Serpiginous choroiditis
Undifferentiated choroiditis
Undifferentiated retinal vasculitis
Panuveitis Syphilitic panuveitis Behçet disease uveitis Sympathetic ophthalmia
Tuberculous panuveitis Undifferentiated panuveitis with choroiditis
Sarcoidosis-associated panuveitis Undifferentiated panuveitis with retinal vasculitis
Vogt-Koyanagi-Harada disease (Early-stage and late-stage)

Adapted from Standardization of Uveitis Nomenclature (SUN) Working Group. Development of classification criteria for the uveitides. Am J Ophthalmol 2021;228:96–116. Used with permission.

Infectious uveitides refer to those with evidence of active infection. They do not include auto-inflammatory or auto-immune diseases triggered by a prior infection (e.g. reactive arthritis-associated uveitis).