Table 1:
Selected Uveitic Diseases†
| Anatomic class | Infectious‡ | Systemic Disease Associated | Eye-limited |
|---|---|---|---|
| Anterior | Cytomegalovirus anterior uveitis | Juvenile idiopathic arthritis-associated anterior uveitis | Fuchs uveitis syndrome |
| Herpes simplex virus anterior uveitis | Spondyloarthritis/HLA-B27-associated anterior uveitis | Undifferentiated anterior uveitis | |
| Varicella zoster virus anterior uveitis | Tubulointerstitial nephritis with uveitis | ||
| Syphilitic anterior uveitis | Sarcoidosis-associated anterior uveitis | ||
| Intermediate | Syphilitic intermediate uveitis | Multiple sclerosis-associated intermediate uveitis | Pars planitis |
| Sarcoidosis-associated intermediate uveitis | Intermediate uveitis, non-pars planitis type (undifferentiated intermediate uveitis) | ||
| Posterior | Acute retinal necrosis | Sarcoidosis-associated panuveitis | Acute posterior multifocal placoid pigment epitheliopathy |
| Cytomegalovirus retinitis | Birdshot chorioretinitis | ||
| Syphilitic posterior uveitis | Multiple evanescent white dot syndrome | ||
| Toxoplasmic retinitis | Multifocal choroiditis with panuveitis | ||
| Tuberculous posterior uveitis | Punctate inner choroiditis | ||
| Serpiginous choroiditis | |||
| Undifferentiated choroiditis | |||
| Undifferentiated retinal vasculitis | |||
| Panuveitis | Syphilitic panuveitis | Behçet disease uveitis | Sympathetic ophthalmia |
| Tuberculous panuveitis | Undifferentiated panuveitis with choroiditis | ||
| Sarcoidosis-associated panuveitis | Undifferentiated panuveitis with retinal vasculitis | ||
| Vogt-Koyanagi-Harada disease (Early-stage and late-stage) |
Adapted from Standardization of Uveitis Nomenclature (SUN) Working Group. Development of classification criteria for the uveitides. Am J Ophthalmol 2021;228:96–116. Used with permission.
Infectious uveitides refer to those with evidence of active infection. They do not include auto-inflammatory or auto-immune diseases triggered by a prior infection (e.g. reactive arthritis-associated uveitis).