Table 2.

Prevalence (%) of sensorineural hearing loss (SNHL) in the different cohorts of patients (d: days; m: months; and y: years).

Authors	SNHL %	Mean Age	Defects
Elander et al. [18]	26.9%	14 y (2d—78)	mtDNA mutations and deletions, and nDNA mutations
van Kempen et al. [19]	35.5%	43 y (18—66)	mtDNA mutations
Sakata et al. [20]	100.0%	40 y (22—66)	mtDNA mutations
Xia et al. [21]	21.0%	7 y (4—9)	mtDNA mutations
Liu et al. [22]	67.1%	27 y (7—66)	mtDNA mutations and deletions
Scarpelli et al. [23]	46.7%	45 y (8—73)	mtDNA mutations and deletions
Nesbitt et al. [24]	51.2%	(11m—74)	mtDNA mutations
Scaglia et al. [25]	39.1%	7 y (6m—83)	mtDNA mutations