TABLE 1.

Underlying common diagnoses of patients with fibrosing interstitial lung diseases (ILDs)

Idiopathic

Idiopathic interstitial pneumonia

Idiopathic non-specific interstitial pneumonia

Cryptogenic organising pneumonia with supervening fibrosis

Idiopathic desquamative interstitial pneumonia

Idiopathic lymphocytic interstitial pneumonia

Non-idiopathic

Connective tissue disease-ILDs

Fibrotic hypersensitivity pneumonitis

Exposure-related ILDs (asbestosis, silicosis, etc.)

Drug-induced ILDs (amiodarone, nitrofurantoin, etc.)

Sarcoidosis

Anti-neutrophilic cytoplasmic auto-antibody-associated vasculitis

Unclassifiable ILD

Although idiopathic pulmonary fibrosis is a progressive and fibrosing ILD, it is a separate, well-defined entity and has not been considered as part of potentially progressive pulmonary fibrosis for this statement.