Table 2.
Physical activity in children with HCTD.
| ACTIVPALᵀᴹ | HCTD (N = 33) | MFS (N = 25) | LDS (N = 2) | EDS (N = 6) |
|---|---|---|---|---|
| Sedentary time in hours, median (IQR) | 9.2 (7.6–10.4) | 8.7 (7.4–10.1) | 11.0 (9.5–n.a.) | 9.4 (8.0–11.0) |
| Active time in hours, median (IQR) | 4.5 (3.5–5.2) | 4.5 (3.5–5.2) | 3.2 (2.7–n.a.) | 4.2 (4.0–5.2) |
| Hours of sleep, median (IQR) | 11.2 (9.5–11.5) | 11.2 (9.8–11.9) | 10.3 (9.7–n.a) | 10.3 (8.5–11.4) |
| Steps/day, median (IQR) | 8351.7 (6456.9–10,484.6) | 8527.9 (6779.1–10,429.6) | 6575.6 (6456.6–n.a.) | 8419.1 (6142.6–14,906.1) |
| PEDI-CAT | HCTD (N = 41) | MFS (N = 24) | LDS (N = 4) | EDS (N = 13) |
| Mobility t-score, mean (SD) | 36.2 (16.1) | 39.0 (15.6) | 30.0 (21.7) | 33.2 (15.7) |
| Z-score | −1.4 (1.6) | −1.1 (1.6) | −2.0 (2.2) | −1.7 (1.6) |
HCTD, heritable connective tissue disorders; MFS, marfan syndrome; LDS, loeys-dietz syndrome; EDS, ehlers-danlos syndromes; PEDI-CAT, pediatric evaluation of disability inventory computer adaptive test; ActivPAL, an accelerometer-based activity monitor; n.a, not applicable due to small sample size.