Table 3.
Physical fitness in children with HCTD.
| HCTD (N = 56) | MFS (N = 37) | LDS (N = 6) | EDS (N = 13) | |
|---|---|---|---|---|
| FTT | ||||
| Time to exhaustion in minutes, mean (SD) | 8.9 (2.8) | 8.8 (2.9) | 8.3 (1.5) | 9.4 (3.1) |
| Z-score, mean (SD) | −3.3 (3.2) | −3.0 (2.9) | −4.2 (2.6) | −3.6 (4.0) |
| HGD | ||||
| dominant hand in kg, mean (SD) | 18.1 (8.0) | 18.2 (8.6) | 17.0 (6.8) | 18.3 (7.5) |
| Z-score, mean (SD) | −1.1 (1.2) | −.85 (1.6) | −1.7 (.57) | −1.5 (.80) |
| Non dominant hand in kg, mean (SD) | 15.7 (7.7) | 15.9 (8.4) | 14.7 (5.1) | 15.6 (6.9) |
| Z-score, mean (SD) | −1.9 (1.0) | −1.8 (1.2) | −2.2 (.55) | −2.0 (.91) |
| BOTMP-2 | ||||
| Fine manual control | ||||
| Standard scores, mean (SD) | 50.2 (9.8) | 50.3 (10.6) | 49.7 (8.3) | 50.0 (8.6) |
| Z-score, mean (SD) | .02 (.98) | .03 (1.1) | −.02 (.83) | .00 (.86) |
| Manual coordination | ||||
| Standard scores, mean (SD) | 49.5 (8.5) | 49.7 (9.2) | 53.0 (8.6) | 47.4 (5.8) |
| Z-Score, mean (SD) | −.05 (.85) | −.03 (.92) | .30 (.86) | −.26 (.58) |
| Body coordination | 47.0 (9.6) | 49.1 (10.2) | 43.5 (6.7) | 42.8 (7.1) |
| Standard scores, mean (SD) | −.30 (.96) | −.09 (1.02) | −.65 (.67) | −.72 (.71) |
| Z-score, mean (SD) | ||||
| Strength and agility | ||||
| Standard scores, mean (SD) | 47.1 (7.7) | 47.1 (8.7) | 46.8 (6.1) | 47.3 (5.6) |
| Z-score, mean (SD) | −.29 (.77) | −.29 (.84) | −.32 (.62) | −.27 (.56) |
| Total test score | ||||
| Standard scores, mean (SD) | 47.6 (9.1) | 48.9 (10.3) | 46.2 (9.1) | 45.3 (5.4) |
| Z-score, mean (SD) | −.24 (1.0) | −.11 (1.03) | −.38 (.61) | −.53 (.54) |
HCTD, heritable connective tissue disorders; MFS, marfan syndrome; LDS, loeys-dietz syndrome; EDS, ehlers-danlos syndromes; FTT, fitkids treadmill test; HGD, handgrip dynamometry; BOTMP-2, the bruininsk-oseretsky test of motor proficiency-2; kg, kilogram; N, numbers; SD, standard deviation.