Table 1.
Details of the mouse models and samples used in this study
| Model and Genotype | Renal Phenotype | Sex |
|---|---|---|
| Pkd1 iKO | ||
| P12 (DPD 1), Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | One female, two males |
| P12 (DPD 1), Pkd1fl/fl:TetO-Cre | Noncystic | One female, two males |
| P14 (DPD 3), Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | One female, two males |
| P14 (DPD 3), Pkd1fl/fl:TetO-Cre | Noncystic | Two females, one male |
| P15 (DPD 4), Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | Two females, one male |
| P15 (DPD 4), Pkd1fl/fl:TetO-Cre - cystic | Noncystic | Two females, one male |
| P20 (DPD 9), Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | Two females, one male |
| P20 (DPD 9), Pkd1fl/fl:TetO-Cre | Noncystic | One female, two males |
| P25, Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | Three males |
| P25, Pkd1fl/fl:TetO-Cre | Noncystic | Two females, one male |
| P150, Pkd1fl/fl:Pax8-rTTa:TetO-Cre | Cystic | Three males |
| P150, Pkd1fl/fl:TetO-Cre | Noncystic | Three males |
| Flcn KO | ||
| P7, Flcnfl/fl:Ksp-Cre | Cystic | Two females, one male |
| P7, Flcnfl/+:Ksp-Cre | Noncystic | One female, two males |
| P14, Flcnfl/fl:Ksp-Cre | Cystic | One female, two males |
| P14, Flcnfl/+:Ksp-Cre | Noncystic | Three females |
| P18, Flcnfl/fl:Ksp-Cre | Cystic | Two females, one male |
| P18, Flcnfl/+:Ksp-Cre | Noncystic | Three males |
| Fnip1/2 dKO | ||
| P18, Fnip1fl/fl:Fnip2fl/fl:Ksp-Cre | Cystic | Three males |
| P18, Fnip1fl/+:Fnip2fl/+:Ksp-Cre | Noncystic | Two females, one male |
dKO, double knockout; DOX, doxycycline; DPD, days post-DOX; KO, knockout P, postnatal day.