Table 1.

Patient demographic data and clinical features.

Patient number	Age of onset (years)	Disease duration (months)	PRNP genotype at codon 129	sCJD subtype	Clinical signs at onset	Western blot: relative occipital PrPSc levels*	MRI: occipital cortex abnormalities
1	60	20	MV	1–2	Visuospatial	0.09	yes
2	55	24	MV	1–2	Behavior	0.6	no
3	69	6	MV	1	Behavior/Memory	3.9	no
4	57	4	MM	1	Motor	3.2	no
5	69	10	MM	1–2	Cognitive/Apraxia	2.3	yes
6	69	15	MV	2	Behavior/Memory	0.9	no
7	56	10	MM	1–2	Language	1.2	no
8	79	27	MV	2	Cognitive	1.1	yes

^*Levels relative to a control case (PrP codon 129 MM1).