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. 2022 Nov 22;58(2):577–584. doi: 10.1002/ppul.26243

Table 4.

Individual patient data on CFTR mutations and VO2 values

Patient CFTR Mutations Peak VO2 (ml/min)a Peak VO2/kga Peak VO2 (% pred)a
1/M F508del/W1282X 2658/2798 41.86/43.05 85/90
2/F F508del/G542X 1379/1652 25.16/29.5 71/86
3/F F508del/W1282X 1822/1762 31.41/30.91 87/92
4/M F508del/F508del 1066/1574 17.77/24.29 37/52
5/M F508del/Y1014C 2350/2226 42.96/41.38 91/86
6/M R1158X/G85E 2133/1746 36.78/27.28 73/58
7/F G85E/G85E 1090/1272 32.06/30.5 87/86

Abbreviations: CFTR, Cystic fibrosis transmembrane regulator; F, female; kg, kilograms; M, male; min, minute; ml, milliliters; pred, predicted; VO2, oxygen uptake.

a

Before/after Trikafta.