Figure 2.

Spectrum of disease scores in 141 children with primary ciliary dyskinesia (PCD) using the (A) Melbourne-Rotterdam annotated grid morphometric analysis (MERAGMA)-PCD CT scoring system and (B) stratified by ciliary ultrastructural defect inner dynein arm/microtubular disorganization (IDA/MTD) versus (C) other. Stacked bar plots showing the wide spectrum of disease scores found by the MERAGMA-PCD scoring system. Participants are sorted on the basis of the total score percentage. %Disease for each patient is subdivided by the subscores %Bronchiectasis, %Mucus plugging, %Airway wall thickening, and %Atelectasis. (A) All children enrolled. (B) Children with PCD and IDA/MTD ciliary ultrastructural defects. (C) Children with PCD and all other ciliary ultrastructural defects. CT = computed tomography.