Table 3.

Baseline computed tomography scores in 141 children with primary ciliary dyskinesia, stratified by ciliary ultrastructural defect group

	All (N = 141)	ODA (n = 57)	ODA/IDA (n = 20)	IDA/MTD (n = 40)	Normal/Near Normal (n = 24)
Atelectasis (%), mean (SD), range	1.6 (1.8) 1–15.2	1.4 (1.3) 0–5.6	1.7 (1.7) 0–6.6	1.6 (1.4) 0–15.2	1.7 (3.1) 0–15.2
Bronchiectasis (%), mean (SD), range	1.5 (0.9) 0–4.1	1.6 (0.9) 0.2–4.1	1.7 (0.8) 0.4–2.9	1.6 (0.8) 0.2–3.6	1.2 (1.0) 0–3.5
Bronchial wall thickening (%), mean (SD), range	0.4 (0.2) 0–1.0	0.4 (0.2) 0–0.8	0.5 (0.2) 0.2–1.0	0.3 (0.2) 0.1–0.7	0.3 (0.2) 0–0.8
Mucus plugging (%), mean (SD), range	1.2 (2.4) 0–14.0	0.5 (1.1) 0–6.2	0.9 (2.1) 0–8.4	2.3 (3.7) 0–14	1.1 (1.6) 0–4.6
Disease (%)*, mean (SD), range	4.6 (3.5) 0.2–19.6	3.8 (2.4) 0.6–12.7	4.7 (2.9) 0.9–12.1	5.9 (4.3) 0.8–18.3	4.3 (4.1) 0.2–19.6

Definition of abbreviations: IDA = inner dynein arm; MTD = microtubular disorganization; ODA = outer dynein arm; SD = standard deviation.

^*Disease (%) is the sum of atelectasis (%), bronchiectasis (%), airway wall thickening (%), and mucus plugging (%).