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. 2023 Mar 31;38(2):e485. doi: 10.5001/omj.2023.64

Table 5. Review of treatments and survival outcomes of patients with biliary atresia in studies published after 2010.

Country of study Author, year Study period No. of patients Sex ratio (M:F) Procedure Median age at HPE, days Native liver survival, year (%) Overall survival,
year (%)
Middle East
Bahrain (present study) Isa et al, 2023 1993–2021 26 11:15 HPE: 23, LT: 3 61 5 (53.8) 5 (65.4)
Saudi Arabia Holdar et al,14 2019 2008–2015 21 11:10 HPE: 12, LT: 9 73 4 (14.3) 4 (81)
Saudi Arabia Khayat et al,15 2021 1999–2017 23 10:13 HPE 77 (56) (69.5)
Iran Naghashi et al,16 2020 2006–2017 90 44:50 HPE: 71 64.7 5 (40) NR
Egypt Gad et al,17 2021 2000–2019 410 186:224 HPE 65 5 (49.8) 5 (51.5)
Asia-Pacific
Hong Kong Chung et al,18 2021 1980–2017 231 97:134 HPE 59 10 (70.7) NR
China Wang et al,30 2019 2009–2012 139 77:62 HPE 78.3 5 (58) NR
India Redkar et al,31 2017 2000–2014 121 75:46 HPE 96 1 (43.8) NR
Europe
Italy Parolini et al,32 2019 1975–1996 174 91:83 HPE 60 5 (41) NR
Nordic countries Pakarinen et al,20 2018 2005–2016 154 71:83 HPE: 148, LT: 6 64 5 (53) 5 (88)
Netherlands de Vries et al,5 2012 1987–2008 214 110:104 HPE 59 4 (46 ± 4) 4 (73 ± 3)
France Chardot et al,8 2013 1986–2009 1107 NR HPE: 1044 59 5 (40) 5 (81)
England and Wales Davenport et al,33 2011 1999–2009 443 NR HPE: 424, LT: 15 54 5 (46) 5 (90)
Africa
South Africa De Maayer et al,34 2017 2009–2012 70 13:30 HPE: 43 64 2 (32.6) NR

mean days; no record; HPE: hepatic portoenterostomy (Kasai procedure); M:F: male:female; LT: liver transplant.