Fig. 2. Audiological data of the proband and her sister.
Hearing thresholds at standard audiometric frequencies are shown for air conduction (cross: left ear, open circle: right) and masked bone conduction (open square to left: left ear, open square to right: right ear) of the proband (A) and her sister (B). Speech audiometry shows the percentage of correct word perception at varying presentation level (dB HL, hearing level) in the proband (C) and her sister (D). Tympanometry in the sister (E) demonstrates a Type C profile (conductive hearing loss) in the right ear, and Type A (normal) in the left ear. MEP: middle ear pressure, ECV: ear canal volume, SC: static compliance.