ACTB	actin beta
ANOVA	one-way analysis of variance
A1R	adenosine A1 receptor
A2AR	adenosine A2A receptor
A2BR	adenosine A2B receptor
A3R	adenosine A3 receptor
ARE	antioxidant response element
ATP	adenosine triphosphate
BSO	L-buthionine sulfoximine
cDNA	complementary DNA
CNS	central nervous system
COX1	cytochrome c oxidase subunit 1
CO2	carbon dioxide
DMEM	Dulbecco’s Modified Eagle Medium
DMSO	dimethyl sulfoxide
FBS	fetal bovine serum
FDA	Food Drug and Administration
Fe-S	Iron–sulfur
FRDA	Friedreich’s ataxia
FXN	frataxin
GAA	guanine–adenine–adenine
h	hour
HMEC-1	human microvascular endothelial cells
H2O2 HSD LHON	hydrogen peroxide Tukey’s honestly significant difference Leber’s hereditary optic neuropathy
mM	millimolar
MMP/ΔΨm	mitochondrial membrane potential
mtDNA	mitochondrial DNA
MTT	3-(4,5-dimethylthiazol-2-yl)-2,5-diphenyltetrazolium bromide
nDNA	nuclear DNA
NFE2L2 NIGMS	NFE2-like bZIP transcription factor 2 National Institute of General Medical Sciences
NRF1	nuclear respiratory factor 1
PC-12	rat pheochromocytoma
PPARGC1A	PPARG coactivator 1 alpha
RNA	ribonucleic acid
ROS	reactive oxygen species
RT-qPCR	reverse transcription quantitative real-time polymerase chain reaction
SD	standard deviation
SDH-A	succinate dehydrogenase subunit A
TFAM	transcription factor A, mitochondrial
TNF-α	tumor necrosis factor alpha
v/v	volume/volume
µM	micromolar
°C	degree Celsius