Table 2.
Values of LCI, spirometric parameters, and the modified Reiff score.
| Total (n = 20) | PCD-BE (n = 9) | nCFnPCD-BE (n = 11) |
|
|---|---|---|---|
| Median LCI (range) | 7 (5–9.1) | 7.3 (6.4–7.8) | 6.8 (5–9.1) |
| Abnormal LCI (%) | 9 (55) * | 6 (66.7) | 3 (27.3) |
| Median FEV1 z-score (range) | −0.6 (−2.4–1.3) | −0.5 (−1.2–0.2) | −0.8 (−2.4–1.3) |
| Abnormal FEV1 z-score (%) | 2 (10) | 0 | 2 (18.2) |
| Median FVC z-score (range) | 0 (−1.9–1.5) | 0.04 (−0.6–0.9) | −0.5 (−1.9–1.5) |
| Abnormal FVC z-score (%) | 1 (5) | 0 | 1 (9.1) |
| Median FEF 25–75% z-score (range) | −0.9 (−2.9–−0.1) | −0.9 (−2.1–−0.1) | −0.8 (−2.9–0.3) |
| Abnormal FEF 25–75% z-score (%) | 3 (15) | 2 (22.2) | 1 (9.1) |
| Median modified Reiff score (range) | 3 (1–7) | 3.5 (1–7) | 2 (1–7) |
* Among the patients with abnormal LCI, the median index was 7.4, with a range between 7.2 and 9.1. Abbreviations: n = number; LCI = lung clearance index; FEV1 = forced expiratory volume in one second; FVC = forced vital capacity; FEF 25–75% = forced expiratory flow at 25–75%; PCD-BE = primary ciliary disease bronchiectasis; nCFnPCD-BE = non-cystic fibrosis, non-primary ciliary disease bronchiectasis.