Figure 4.

HRCT scan of a 42-year-old female pSS patient in 2008 (A) showing only very modest signs of bronchiolitis. She went on to experience recurrent episodes of acute dyspnea and cough, and follow-up HRCT scans in 2011 (B) and 2021 (C) document progressive formation of thin-walled cysts. The combination of these imaging findings and appropriate clinical context in a pSS patient is virtually pathognomonic of LIP. Of note, confluence of LIP cystic lesions into larger ones (as is shown in (C)) exposes the patient to higher risk of complications.