Table 1.

Subtypes of PCLs according to WHO-EORTC classification 2018 and changes according to International Consensus Classification (ICC) of Mature Lymphoid Neoplasms 2021 [4,19].

Entity	Disease	Changes in ICC, 2021
CTCL	MF MF variants   Folliculotropic MF   Pagetoid reticulosis   Granulomatous slack skin SS Adult T-cell leukemia/lymphoma Primary cutaneous CD30+ LPDs   C-ALCL   LyP Subcutaneous panniculitis-like T-cell lymphoma Extranodal NK/T-cell lymphoma, nasal type Chronic active EBV infection Primary cutaneous peripheral T-cell lymphoma, rare subtypes   Primary cutaneous γ/δ T-cell lymphoma   CD8+ AECTCL (provisional)   Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (provisional)   Primary cutaneous acral CD8+ T-cell lymphoma (provisional) Primary cutaneous peripheral T-cell lymphoma, NOS	Primary cutaneous acral CD8+ T-cell LPD
CBCL	PCMZL PCFCL PCDLBLC, LT EBV+ mucocutaneous ulcer (provisional) Intravascular large B-cell lymphoma	Primary cutaneous marginal zone LPD

MF: mycosis fungoides; SS: Sezary syndrome; LPD: lymphoproliferative disorder; C-ALCL: cutaneous anaplastic large cell lymphoma; LyP: lymphomatoid papulosis; CD8⁺ AECTCL: primary cutaneous aggressive epidermotropic CD8⁺ cytotoxic T-cell lymphoma; PCMZL: primary cutaneous marginal zone lymphoma; PCFDL: primary cutaneous follicle center lymphoma; PCDLBCL, LT: primary cutaneous diffuse large B-cell lymphoma, leg type.