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. 2023 Jan 7;25(6):1017–1028. doi: 10.1093/neuonc/noad002

Table 2.

Representative Recent Phase ≥ II Clinical Trials for Recurrent GBM Patients Evaluating Non-angiogenic, Biologic-Based Therapeutics

Agent # Patients Response
Criteria
# Recurrences Primary trial endpoint ORR (%) mOS
[Weeks]
Citation
Rilotumumab 61 Macdonald ≤3 ORR 0 23.5 Wen et al50
 Cilengitide 81 Macdonald ≤1 PFS6 9 43 Reardon et al57
 Enzastaurin 174 Levin ≤2 PFS 2.9 28.7 Wick et al39
 Erlotinib 54 Macdonald ≤1 PFS6 3.7 33.5 van den Bent et al58
 Erlotinib 48 WHO ≤1 ORR 6.3 42.1 Yung et al59
 Erlotinib + sirolimus 32 Macdonald 1 PFS6 0 33.8 Reardon et al51
 Fenretinib 23 Not stated ≤2 PFS6 0 30 Puduvalli et al52
 Imatinib 51 Macdonald ≤2 ORR or PFS6 5.9 23 Raymond et al60
 Imatinib + hydroxyurea 33 Macdonald No limit PFS6 9 48.9 Reardon et al61
 Imatinib + hydroxyurea 231 Macdonald 1 ORR 3.4 26 Reardon et al62
 Imatinib + hydroxyurea 120 Macdonald 1 PFS 1.7 21 Dresemann et al34
Temsirolimus 65 Macdonald ≤2 PFS6 0 19 Galanis et al53
 Vorinostat 66 Macdonald ≤2 ORR 3.0 24.8 Galanis et al43
 Perifosine 16 RANO No limit PFS6 0 14.7 Kaley et al54
 Buparlisib 65 RANO ≤2 PFS6 0 42.6 Wen et al55
 Marizomib 30 RANO ≤2 ORR 3.3 39.5 Bota et al63
 Selinexor 68
(24 50 mg 2xWK)
(14, 60 mg 2xWK)
(30, 80 mg 1xWK)
RANO ≤3 PFS6 8.3 (50 mg) 7.7 (60 mg)
10 (80 mg)
45.6
33.5
43.5
Lassman et al64
Dabrafenib + trametinib (in BRAF mutant rGBM)* 31 RANO 1 ORR 32 59.5 Wen et al56

Believed to be a “positive” study, with ORR = 32% and mOS of more than a year.

*Note this involved an enriched patient population.

PFS = Progression-free survival.

PFS6 = Proportion of patients with PFS at or beyond 6 months from start of treatment (or randomization).

OS = Overall survival.