TABLE 5.
RBANS-H Subscale Scores for DFNA9 and control subjects
| RBANS-H Subscales | DFNA9 Patients (n = 46) (mean ± SD) | Control Subjects (n = 46) (mean ± SD) | WS | z | p |
|---|---|---|---|---|---|
| Immediate Memory | 107.83 ± 14.01 | 116.24 ± 14.73 | 1752.0 | −3.03 | 0.003 * |
| Visuospatial/Constructional | 96.30 ± 17.02 | 104.22 ± 10.87 | 1880.0 | −2.03 | 0.043* |
| Language | 102.57 ± 12.50 | 102.91 ± 10.53 | 2096.0 | −0.33 | 0.740 |
| Attention | 94.87 ± 15.70 | 101.89 ± 13.85 | 1836.0 | −2.37 | 0.018* |
| Delayed Memory | 102.11 ± 11.93 | 105.63 ± 16.49 | 1824.0 | −2.46 | 0.014* |
| Total Scale | 101.28 ± 15.68 | 109.54 ± 10.98 | 1750.0 | −3.04 | 0.002 * |
DFNA9 patients scored significantly worse on all subscales, except for the Language subscale, compared with the control group.
indicates statistical significance (α = 0.05), p values in bold indicate statistical significance after Bonferroni correction (α = 0.008).
DFNA9, DeaFNess Autosomal dominant 9; RBANS-H, Repeatable Battery for the Assessment of Neuropsychological Status, adjusted for the Hearing Impaired.