Table 2.
The pathological characteristics of PIS patients.
| Case no. | Dianosis | Grade | CK | SMA | Desmin | CD34 | CD99 | SATB2 | TLE1 | MDM2 | SSTR-2 | S-100 | Myogenin | Ki-67 (%) | NGS |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | adult fibrosarcoma | G1 | – | focal+ | – | – | NA | NA | NA | NA | – | – | – | 30 | NA |
| 2 | adult fibrosarcoma | G1 | – | – | – | + | – | NA | – | – | – | 20 | ETV::NTRK3 (-) | ||
| 3 | myxofibrosarcoma | G2 | – | – | – | – | – | + | + | + | – | – | – | 25 | Mutation of NRAS, PIK3CA, BAP1, KDR, BLMT |
| 4 | undifferentiated pleomorphic sarcoma | G3 | – | – | – | – | – | NA | – | – | – | 30 | NA | ||
| 5 | undifferentiated round cell sarcoma | G3 | – | – | – | – | + | NA | NA | – | – | – | – | 85 | NA |
| 6 | leiomyosarcoma | G3 | – | + | + | NA | NA | NA | NA | NA | – | – | – | 50 | NA |
| 7 | extraskeletal myxoid chondrosarcoma | G3 | – | – | – | – | NA | NA | NA | NA | NA | – | – | 50 | NA |
| 8 | angiosarcoma | G2 | – | NA | NA | + | NA | NA | NA | NA | – | NA | NA | 30 | NA |
| 9 | mesenchymal chondrosarcoma |
G2 | NA | NA | NA | – | NA | – | NA | NA | NA | NA | NA | 40 | NA |
| 10 | undifferentiated spindle cell sarcoma | G1 | – | – | – | – | – | + | + | NA | + | – | – | 10 | Mutation of PBRM1, TOP2A, DUSP2 CNV deletions of SMAR SH3BP5::RAF1 gene fusion |
| 11 | chondrosarcoma | G1 | – | – | – | – | NA | NA | NA | NA | + | + | NA | 2 | NA |
| 12 | chondrosarcoma | G1 | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA |
| 13 | chondrosarcoma | G1 | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA |
| 14 | chondrosarcoma | G1 | – | – | – | – | NA | NA | NA | NA | NA | NA | NA | 3 | NA |