Table 1.

Demographic profile, clinical presentation, family history, operative intervention and follow up of patients of Peutz Jegher’s syndrome

Case number	Age (years)/sex	Presentation
		Obstruction	Intussusception	Bleeding PR	Melanosis	Family history	Surgery	Follow up
1	12/female	Present, previously misdiagnosed as malrotation and Koch’s abdomen	Ileocolocolic	Present	Present [Figure 2]	Present, mother and 3 siblings [Figure 1]	Ileostomy with biopsy, followed by endoscopic polypectomy then multiple enterotomies with removal of polyp [Figure 3]	Doing well
2	21/female	Present	Ileocolocolic	Present	Present	Present	Ileotransverse anastomosis 3 years back	Doing well
3	17/female	present	Ileocolocolic	Present	Present	Present	Ileotransverse anastomosis 7 years back	Doing well
4	10/female	Absent	Absent	Present	Present	Present	Not operated	Doing well
5	55/female	Absent	Absent	present	present	Present	Coloscopy showed polyposis	Doing well
6	8/male	Present, misdiagnosed as malrotation previously	Ileocolocolic	Present	Present, being treated with dermatologist for 2 years	Present, father	Ileoascending anastomosis	Doing well
7	38/male	Absent	Absent	Present	Present	Present	Colonoscopy and upper GI endoscopy showed polyposis	Doing well
8	8/male	Present	Jejunojejunal [Figure 4]	Present	Present	Lost to follow up	Jejunojejunal anastomosis	Doing well
9	8/male	Present	Ileocolocolic	Present	Present	Lost to follow up	Ileoascending anastomosis	Doing well
10	9/male	Present	Ileocolocolic	Present	Present	Present	Ileoascending anastomosis	Doing well
11	7/male	Present	Jejunojejunal	Present	Present	Present	Jejunojejunal anastomosis	Doing well

PR: Per rectal, GI: Gastrointestinal