Table 2.
Rare cancers of India with incidence ≤6/1,00,000 populations.
| ICD code | Cancer site | Total number | Percentage | AAR | CR | 95% CI |
|
|---|---|---|---|---|---|---|---|
| Lower | Upper | ||||||
| C56 | Ovary | 4972 | 3.0 | 5.9 | 5.7 | 5.50 | 5.81 |
| C03-06 | Mouth | 9439 | 5.6 | 5.6 | 5.2 | 5.10 | 5.31 |
| C15 | Oesophagus | 8887 | 5.3 | 5.6 | 4.9 | 4.80 | 5.00 |
| C 61 | Prostate | 4287 | 2.6 | 5.8 | 4.6 | 4.73 | 4.45 |
| C16 | Stomach | 6899 | 4.1 | 4.3 | 3.8 | 3.71 | 3.89 |
| C01-02 | Tongue | 6460 | 3.9 | 3.9 | 3.6 | 3.47 | 3.65 |
| Cancers with incidence ≤3/1,00,000 population | |||||||
| C54-55 | Corpus uteri and uterus uns | 3010 | 1.8 | 3.8 | 2.8 | 2.65 | 2.87 |
| C23-24 | Gallbladder etc. | 4973 | 3.0 | 3.1 | 2.7 | 2.67 | 2.82 |
| C22 | Liver | 4452 | 2.7 | 2.8 | 2.5 | 2.38 | 2.53 |
| C82-85 | Non-Hodgkin lymphoma | 4411 | 2.6 | 2.7 | 2.4 | 2.36 | 2.50 |
| C32 | Larynx | 4295 | 2.6 | 2.7 | 2.4 | 2.30 | 2.44 |
| C19-20 | Rectum | 4039 | 2.4 | 2.5 | 2.2 | 2.16 | 2.30 |
| C18 | Colon | 4024 | 2.4 | 2.5 | 2.2 | 2.15 | 2.29 |
| C73 | Thyroid | 4023 | 2.4 | 2.1 | 2.2 | 2.15 | 2.29 |
| C70-72 | Brain, nervous system | 3632 | 2.2 | 2.1 | 2.0 | 1.94 | 2.07 |
| C12-13 | Hypopharynx | 3308 | 2.0 | 2.1 | 1.8 | 1.76 | 1.89 |
| C67-68 | Ureter, bladder, uns urinary organs | 3059 | 1.8 | 2.0 | 1.7 | 1.61 | 1.76 |
| C92-C94 | Myeloid Leu. | 2999 | 1.8 | 1.7 | 1.7 | 1.59 | 1.71 |
| C09-10 | Tonsil and oth oropharynx | 2292 | 1.4 | 1.4 | 1.3 | 1.19 | 1.34 |
| C91 | Lymphoid Leu. | 2222 | 1.3 | 1.4 | 1.2 | 1.17 | 1.28 |
| C44 | Skin | 2149 | 1.3 | 1.3 | 1.2 | 1.13 | 1.23 |
| C25 | Pancreas | 2125 | 1.3 | 1.3 | 1.2 | 1.12 | 1.22 |
| C90 | Multiple Myeloma | 1983 | 1.2 | 1.3 | 1.1 | 1.05 | 1.14 |
| C64 | Kidney | 1942 | 1.2 | 1.2 | 1.1 | 1.02 | 1.12 |
| Cancers with incidence ≤1/1,00,000 population | |||||||
| C40-41 | Bone | 1709 | 1 | 1 | 0.9 | 0.90 | 0.99 |
| C47,C49 | Connective and soft tissue | 1473 | 0.9 | 0.9 | 0.8 | 0.77 | 0.85 |
| C 60 | Penis | 753 | 0.5 | 0.5 | 0.8 | 0.86 | 0.75 |
| C81 | Hodgkin disease | 1163 | 0.7 | 0.6 | 0.6 | 0.60 | 0.68 |
| C11 | Nasopharynx | 1091 | 0.7 | 0.6 | 0.6 | 0.57 | 0.64 |
| C62-63 | Testis and other MGO | 583 | 0.3 | 0.6 | 0.6 | 0.69 | 0.56 |
| C52, C57 | Vagina and other FGO | 406 | 0.2 | 0.5 | 0.5 | 0.52 | 0.40 |
| C07-08 | Salivary glands | 798 | 0.5 | 0.5 | 0.4 | 0.41 | 0.47 |
| C14 | Pharynx uns. | 645 | 0.4 | 0.4 | 0.4 | 0.33 | 0.38 |
| C95 | Leu uns. | 610 | 0.4 | 0.4 | 0.3 | 0.31 | 0.36 |
| C51 | Vulva | 291 | 0.2 | 0.4 | 0.3 | 0.37 | 0.29 |
| C21 | Anus and Anal Canal | 547 | 0.3 | 0.3 | 0.3 | 0.28 | 0.33 |
| C30-31 | Nose, sinuses etc. | 545 | 0.3 | 0.3 | 0.3 | 0.28 | 0.33 |
| C00 | Lip | 506 | 0.3 | 0.3 | 0.3 | 0.25 | 0.30 |
| C43 | Melanoma of skin | 504 | 0.3 | 0.3 | 0.3 | 0.25 | 0.30 |
| C17 | Small intestine | 389 | 0.2 | 0.2 | 0.2 | 0.19 | 0.24 |
| C37-38 | Oth. thoracic organs | 296 | 0.2 | 0.2 | 0.2 | 0.14 | 0.18 |
| Cancers with incidence ≤0.1/1,00,000 population | |||||||
| C69 | Eye | 269 | 0.2 | 0.2 | 0.1 | 0.13 | 0.17 |
| C74 | Adrenal gland | 140 | 0.1 | 0.1 | 0.1 | 0.06 | 0.09 |
| C58 | Placenta | 67 | 0.0 | 0.1 | 0.1 | 0.09 | 0.06 |
| C96 | Oth malignancies of lymphoid, hematopoietic and related tissues | 98 | 0.1 | 0.1 | 0.1 | 0.04 | 0.06 |
| C65 | Renal pelvis | 17 | 0.0 | 0.0 | 0.0 | 0.00 | 0.01 |
| C88 | Malig IPD | 16 | 0.0 | 0.0 | 0.0 | 0.00 | 0.01 |
| C45 | Mesothelioma | 15 | 0.0 | 0.0 | 0.0 | 0.00 | 0.01 |
| C46 | KS | 9 | 0.0 | 0.0 | 0.0 | 0.00 | 0.01 |
Cancers listed in italics represent the ultra-rare cancers with incidence <0.1/1,000,000 population.51
AAR Age-adjusted rate, CI confidence interval, CR Crude rate, FGO Female genital organs, ICD International Classification of Diseases, KS Kaposi sarcoma, Leu Leukemia, Malig IPD Malignant immunoproliferative disorder, MGO male genital organs, Oth Other, uns unspecified.