Table 1.
Clinical characteristics | ARVC GE patients (n = 8) | ARVC PKP2 patients (n = 8) | p-value |
---|---|---|---|
| |||
Male | 2 (25) | 2 (25) | - |
Age at CMR, years | 31.0 [22–45] | 35.3 [18–55] | 0.55 |
Age at first clinical VT, years | 34.0 [22–45] | 31.0 [17–55] | 0.94 |
ICD implantation | 7 (88) | 7 (88) | - |
Beta blocker | 8 (100) | 5 (63) | 0.056 |
Sodium channel blocker | 2 (25) | 3 (38) | 0.59 |
Syncope | 2 (25) | 2 (25) | - |
| |||
Cardiac function | |||
| |||
RV hypokinesis | 4 (50) | 6 (75) | 0.15 |
RVEF (%) | 37.6 ± 5.5 | 36.1 ± 9.7 | 0.76 |
RVCO (L/min) | 4.7 ± 1.2 | 4.9 ± 0.9 | 0.72 |
RVEDVI (ml/m2) | 131.8 ± 31.2 | 144.5 ± 63.3 | 0.66 |
LVEF (%) | 57.2 ± 6.5 | 55.7 ± 10.0 | 0.74 |
LVEDVI (ml/m2) | 89.3 ± 9.2 | 89.7 ± 23.0 | 0.97 |
LVCO (L/min) | 5.1 ± 0.8 | 5.0 ± 0.9 | 0.86 |
Values are given as n%, mean [range], or mean ± standard deviation (SD). p values were calculated using Student’s t-test with p ≤ 0.05 as statistically significant. CMR = cardiac magnetic resonance; VT = ventricular tachycardia; ICD = implantable cardiac defibrillator; RV = right ventricle; LV = left ventricle; RVEF = right ventricular ejection fraction; RVCO = right ventricular cardiac output; RVEDVI = right ventricular end-diastolic volume index; LVEF = left ventricular ejection fraction; LVCO = left ventricular cardiac output; LVEDVI = left ventricular end-diastolic volume index. The cardiac function parameters were obtained from CMR reports.