Urea cycle and its enzymes.
ARG1, arginase 1; ASL, argininosuccinate lyase; ASS1, argininosuccinate synthetase 1; CPS1, carbamoyl phosphate synthetase 1; HCO3-, bicarbonate; NAGS; N-Acetylglutamate synthase; NH3, ammonia; OTC, ornithine transcarbamylase.