Table 1.

Frequency of interstitial lung disease in some connective tissue diseases

Disease	ILD prevalence	Comment
Systemic sclerosis	Up to 80% (on imaging) 30–40% (clinical disease) [3]	+ anti-Scl-70 is a risk factor
Polymyositis/dermatomyositis	Up to 65–78% (imaging and PFTs) [4]	More common with anti-synthetase antibodies
Rheumatoid arthritis	1–73% [5]	Rare in seronegative disease
Systemic lupus erythematosus	3–9% [6]
Sjogren’s syndrome	10–20% [7]