Table 2.

Teaching points

Pre-kidney transplant evaluation of chronic kidney disease patients with a history of nephrolithiasis should include PH screening.

Recurrent oxalate nephropathy can result in rapid allograft failure in PH2 patients after isolated kidney transplantation.

Limited evidence now suggests that liver transplantation provides clinically significant correction of the metabolic abnormality in PH2, but it comes with significant risk of hepatobiliary complications that are associated with this procedure, as our case demonstrates.

If isolated kidney transplantation is contemplated for a PH2 patient, a regimen for treatment of the persistent hyperoxaluria and the risk for recurrent stones and oxalate nephropathy in the perioperative period and beyond is essential.

PH2, Primary hyperoxaluria type 2.