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. Author manuscript; available in PMC: 2023 Jul 11.
Published in final edited form as: Eur Respir J. 2021 Dec 31;59(1):2003337. doi: 10.1183/13993003.03337-2020

FIGURE 1.

FIGURE 1

Distribution of children with pulmonary hypertension (PH) according to the World Symposium on Pulmonary Hypertension (WSPH) classification system. The proportions of subjects with paediatric PH are depicted according to the 2013 WSPH classification (n=1475 subjects). Group 3 disorders (lung or hypoxia-related PH) constitute the largest proportion of subjects in the PPHNet Registry followed closely by Group 1 (pulmonary arterial hypertension (PAH)). CTEPH: chronic thromboembolic PH; PVOD: pulmonary veno-occlusive disease; PCH: pulmonary capillary haemangiomatosis.