Table 4.
Associated malformation and prognosis of UAPA.
| Case | Gestational age (weeks) | Affected PA | Associated with intracardiac malformations | Outcome | The connection of the pulmonary artery on the affected side |
|---|---|---|---|---|---|
| 1 | 26+4 | L | TOF | Termination, dissection | Connected to the lower right side of the transverse arch of the aorta by DA |
| 2 | 22 | L | Right aortic arch with mirrored branches | Termination, dissection | Connected to the LINA by DA; misdiagnosed as AOPA |
| 3 | 22+5 | L | TOF, APVS | Termination, vascular casting | Connected to the transverse arch of the aorta by DA, misdiagnosed as AOPA |
| 4 | 26 | L | TOF | Termination, dissection | Connected to the transverse arch of the aorta by DA, misdiagnosed as AOPA |
| 5 | 24+4 | L | Right aortic arch with mirrored branches | Termination, dissection | Connected to the LINA by DA |
UAPA, unilateral absence of the pulmonary artery; AOPA, anomalous origin of unilateral pulmonary artery; TOF, tetralogy of Fallot; APVS, absent pulmonary valve syndrome; LINA, left innominate artery; DA, ductus arteriosus.