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Table 2. The reported prevalence of cardiac amyloidosis with different presentations.

Conditions Any CA ATTRwt ATTRv
HFpEF 13-17% 17% ATTR deposits (autopsy); 5% moderate to severe deposits; > 80 y 40%, male predominant; < 65 y 0% Varying levels of cardiac involvement by different TTR variants
HF 11.4% in Afro-Caribbean patients, UK 8.5% (V122I) in Afro-Caribbean patients, UK
Severe AS for surgical valve replacement 6-12%
TAVR 8-16%
Degenerative AS  16% 
Low-flow, low-gradient pattern AS  30% 
HCM 5%, France

AS, aortic stenosis; ATTRv, hereditary transthyretin amyloid cardiomyopathy; ATTRwt, wild type transthyretin amyloid cardiomyopathy; CA, cardiac amyloidosis; HCM, hypertrophic cardiomyopathy; HF, heart failure; HFpEF, heart failure with preserved ejection fraction; TAVR, transcatheter aortic valve replacement; TTR, transthyretin; UK, United Kingdom; y, year.