Table 1.

Characteristics of patients.

	All n = 26	Male n = 11	Female n = 15	p-value
Age (years)	11.9 (±5.3)	10.3 (±5.7)	11.8 (±5.0)	0.3663
Weight (kg)	35 (±17.6)	40.8 (±19,5)	27.1 (±12.9)	0.0414
Height (cm)	139.9 (±28.1)	149.2 (±26.6)	127.3 (±27.5)	0.0552
BMI (kg/m2)	16.5 (±2.9)	17.1 (±3.3)	15.7 (±2.4)	0.2233
Age at diagnosis (months*)	14 (4.5–51.8)	17 (5.5–48)	7 (5–46.5)	0.5892
FEV1 (%)	71.5 (±28.4)	84.0 (±21.1)	50,7 (±28.0)	0.1113
Sweat test (mM/L)	54.18 (15.4)	60.0 (±0.0)	55.67 (±8.6)	0.2072

BMI: Body Mass Index, mean (±SD), *median (IQR).