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. 2023 Jun 5;9(6):e17005. doi: 10.1016/j.heliyon.2023.e17005

Table 2.

Clinical features of patients.

Clinical Manifestations n %
Gastrointestinal and Nutritional manifestations
Steatorrhea – malabsorption 17 65.4
Growth failure 9 34.6
Vomiting 3 11.5
Poor appetite 1 3.8
Respiratory manifestations
Bronchial obstructive syndrome 7 26.9
Recurrent pneumonia 12 46.2
Bronchiectasis 1 3.8
Other symptoms
Salty-tasting skin 3 11.5
Dextrocardia 1 3.8