Table 1.

Contraindications for the KD treatment.

Absolute contraindications for the KD	Relative contraindications for the KD
Carnitine deficiency (primary)	The presence of surgical focus as being identified by neuroimaging and video electroencephalogram monitoring
Carnitine palmitoyl-transferase I or II deficiency	Inability to maintain adequate nutrition (fastidious eater)
Carnitine translocase deficiency	Parent or caregiver non-compliance
Pyruvate carboxylase deficiency	Propofol concurrent use (risk of propofol infusion syndrome may be higher)
Porphyria
β-oxidation defects: Short-chain acyl dehydrogenase deficiency Medium-chain acyl dehydrogenase deficiency Long-chain acyl dehydrogenase deficiency Medium-chain 3-hydroxy acyl-CoA deficiency Long-chain 3-hydroxy acyl-CoA deficiency