Table 3.
Visual Acuity, Visual Field, and Legal Blindness Data
| Total | USH1 | MYO7A | CDH23 | USH1C | USH2 | USH2A | ADGRV1 | USH3/CLRN1 | USH4/ARSG | |
|---|---|---|---|---|---|---|---|---|---|---|
| Age (yr) | 43.31 ± 15.76 | 42.74 ± 15.1 | 42.0 ± 15.7 | 44.5 ± 15.7 | 48 | 43.0 ± 15.7 | 43.0 ± 15.6 | 46.3 ± 11.8 | 48 | 84 |
| VA | 130 (89.7%) | 34 (94.4%) | 22 (95.7%) | 6 (85.7%) | 1 (100%) | 94 (88.7%) | 66 (88.0%) | 15 (93.8%) | 1 (100%) | 1 (100%) |
| VA, mean ± SD | 0.47 ± 0.58 | 0.58 ± 0.66 | 0.58 ± 0.68 | 0.23 ± 0.20 | 0.18 | 0.42 ± 0.55 | 0.43 ± 0.53 | 0.37 ± 0.59 | 0.81 ± 0.27 | 0.70 ± 0.42 |
| Better eye ≤0.3 | 82 (63.1%) | 20 (58.8%) | 13 (59.1%) | 6 (100%) | 1 (100%) | 62 (66.0%) | 42 (63.6%) | 12 (80.0%) | 0 | 0 |
| Better eye ≥1.0 | 14 (10.8%) | 5 (25.0%) | 4 (18.2%) | 0 | 0 | 9 (9.6%) | 6 (9.1%) | 1 (6.7%) | 0 | 0 |
| VF | 96 (66.2%) | 29 (80.6%) | 19 (82.6%) | 5 (71.4%) | — | 66 (62.3%) | 48 (64.0%) | 8 (50.0%) | 1 (100%) | — |
| VF, mean ± SD | 31.3° ± 32.8° | 28.8° ± 34.0° | 31.0° ± 35.8° | 39.0° ± 35.7° | — | 31.5° ± 30.2° | 31.5° ± 30.5° | 16.0° ± 12.7° | 20 | — |
| ≤20° | 96 (50.0%) | 35 (60.3%) | 24 (63.2%) | 3 (30.0%) | — | 59 (44.7%) | 40 (41.7%) | 13 (81.3%) | 2 (100%) | — |
| ≤10° | 48 (25.0%) | 14 (24.1%) | 6 (39.5%) | 2 (20.0%) | — | 34 (25.8%) | 22 (22.9%) | 6 (37.5%) | 2 (100%) | — |
| Legal blindness | 50 (34.5%) | 16 (55.2%) | 11 (47.8%) | 1 (14.3%) | 0 | 33 (31.1%) | 23 (30.7%) | 6 (37.5%) | 1 (100%) | 0 |
| LB by VF | 44 (45.8%) | 16 (55.2%) | 11 (57.9%) | 1 (20.0%) | — | 27 (20.5%) | 18 (37.5%) | 6 (37.5%) | 1 (100%) | — |
| LB by VA | 15 (11.5%) | 6 (17.6%) | 5 (22.7%) | 0 | 0 | 9 (9.6%) | 6 (9.1%) | 1 (6.7%) | 0 | — |
| LB by both | 8 (5.6%) | 5 (13.9%) | 4 (17.4%) | 0 | 0 | 3 (2.8%) | 1 (1.3%) | 1 (6.3%) | 0 | — |
LB, legal blindness; SD, standard deviation; VA, visual acuity; VF, visual field.