Table 2.
Characteristics of the example patients shown in Figure 5.
Parameter | Yellow | Green | Cyan | Blue | Orange | Red |
---|---|---|---|---|---|---|
♦ | ||||||
Age (yo) | 20 | 25 | 26 | 38 | 43 | 46 |
ht-TKVp (ml/m) | 277 | 452 | 745 | 979 | 1054 | 1687 |
ht-TCV (ml/m) | 83 | 108 | 439 | 579 | 747 | 1332 |
ht-RPV (ml/m) | 194 | 344 | 307 | 399 | 307 | 355 |
TCN | 52 | 173 | 252 | 283 | 188 | 106 |
CPSA (cm2) | 198 | 588 | 1036 | 1183 | 771 | 569 |
Genotype | PKD1-T | PKD1-T | PKD1-T | PKD1-NT | PKD2-T | PKD1-NT |
● | ||||||
Age (yo) | 18 | 43 | 42 | 26 | 26 | 36 |
ht-TKVp (ml/m) | 263 | 440 | 749 | 929 | 1073 | 1745 |
ht-TCV (ml/m) | 51 | 166 | 322 | 513 | 600 | 965 |
ht-RPV (ml/m) | 212 | 274 | 427 | 415 | 472 | 780 |
TCN | 167 | 229 | 500 | 357 | 453 | 951 |
CPSA (cm2) | 369 | 718 | 1597 | 1636 | 2070 | 4196 |
Genotype | PKD1-T | PKD1-T | PKD1-T | PKD1-T | PKD1-T | PKD1-T |
T: truncating; NT: non-truncating