Table 6.
Summary statistics for SARA, BARS, and Functional Staging slopes (i.e., annual change)
| SCA1 | SCA2 | SCA3 | SCA6 | Overall | |
|---|---|---|---|---|---|
| SARA | |||||
| n | 67 | 74 | 147 | 68 | 356 |
| M (SD) | 1.542 (2.699) | 0.385 (2.909) | 1.2 (3.506) | 0.994 (3.353) | 1.056 (3.228) |
| 95%_CI | [0.884;2.201] | [−0.289;1.059] | [0.628;1.771] | [0.182;1.805] | [0.719;1.392] |
| Progression_slope_[n (%)] | 53 (79.1%) | 44 (59.5%) | 104 (70.7%) | 45 (66.2%) | 246 (69.1%) |
| Non-progression_slope_[n (%)] | 14 (20.9%) | 30 (40.5%) | 43 (29.3%) | 23 (33.8%) | 110 (30.9%) |
| BARS | |||||
| n | 12 | 10 | 14 | 10 | 46 |
| M (SD) | 0.427 (2.805) | −0.556 (2.476) | 1.533 (4.365) | −0.167 (2.637) | 0.421 (3.274) |
| 95%_CI | [−1.356;2.209] | [−2.327;1.215] | [−0.988;4.053] | [−2.054;1.719] | [−0.552;1.393] |
| Progression_slope_[n (%)] | 7 (58.3%) | 5 (50%) | 10 (71.4%) | 4 (40%) | 26 (56.5%) |
| Non-progression_slope_[n (%)] | 5 (41.7%) | 5 (50%) | 4 (28.6%) | 6 (60%) | 20 (43.5%) |
| Functional_staging | |||||
| n | 60 | 68 | 134 | 68 | 330 |
| M (SD) | 0.321 (0.527) | 0.137 (0.374) | 0.132 (0.674) | 0.164 (0.575) | 0.174 (0.578) |
| 95%_CI | [0.185;0.457] | [0.047;0.228] | [0.017;0.247] | [0.025;0.303] | [0.719;1.392] |
| Progression_slope_[n (%)] | 48 (80%) | 49 (72.1%) | 82 (61.2%) | 39 (57.4%) | 218 (66.1%) |
| Non-progression_slope_[n (%)] | 12 (20%) | 19 (27.9%) | 52 (38.8%) | 29 (42.6%) | 112 (33.9%) |
M (SD), mean (standard deviation); CI, confidence interval