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. Author manuscript; available in PMC: 2023 Aug 13.
Published in final edited form as: Pediatr Res. 2023 Feb 13;94(2):691–698. doi: 10.1038/s41390-023-02490-9

Table 5:

Neurodevelopmental outcomes at 30 months of age in children with heterogenous critical congenital heart disease

HLHS TGA Other
All Genetic syndrome No syndrome
Participants with BSID-II follow-up, n= 11 54 14 4 10
Age at follow-up, years, median (IQR) 2.6 (2.5-2.7) 2.6 (2.5-2.7) 2.7 (2.6-2.9) 2.7 (2.7-2.8) 2.7 (2.6-3.0)
p= 0.042 0.515
Mental Developmental Index, median (IQR) 95.0 (81.5-96.0) 93.5 (84.0-104.0) 82.5 (67.0-88.0) 58.5 (50.0-75.5) 85.0 (81.0-101.0)
p= 0.035 0.047
Normal, n= (%) 7 (64%) 40 (74%) 5 (36%) 0 (0%) 5 (50%)
Mild-moderate, n= (%) 2 (18%) 13 (24%) 5 (36%) 1 (25%) 4 (40%)
Severe, n= (%) 2 (18%) 1 (2%) 4 (29%) 3 (75%) 1 (10%)
Psychomotor Developmental Index, median (IQR) 77.0 (71.5-83.5) 91.0 (84.0-102.0) (n=52) 85.5 (76.0-98.0) 54.5 (50.0-68.0) 91.5 (83.0-98.0)
p= 0.008 0.007
Normal, n= (%) 3 (27%) 39 (75%) 7 (50%) 0 (0%) 7 (70%)
Mild-moderate, n= (%) 6 (55%) 10 (19%) 4 (29%) 1 (25%) 3 (30%)
Severe, n= (%) 2 (18%) 3 (6%) 3 (21%) 3 (75%) 0 (0%)