Table 2.
Subject characteristics.
| Parameter (unit) | Statistics/category | Unit (%) | |
|---|---|---|---|
| Age (months) | Number of subjects | 23 | |
| Mean | 9.0 | ||
| Standard deviation | 6.3 | ||
| Maximum | 23 | ||
| Median | 7.0 | ||
| Minimum | 2 | ||
| Sex | Male | 12 | (52.17) |
| Female | 11 | (47.83) | |
| Height | Number of subjects | 23 | |
| Mean | 68.82 | ||
| Standard deviation | 7.88 | ||
| Maximum | 82.3 | ||
| Median | 70.40 | ||
| Minimum | 57.1 | ||
| Weight (kg) | Number of subjects | 23 | |
| Mean | 7.611 | ||
| Standard deviation | 1.651 | ||
| Maximum | 10.21 | ||
| Median | 7.500 | ||
| Minimum | 4.91 | ||
| Ethnicity | Japanese | 23 | (100.00) |
| Race | Asian | 23 | (100.00) |
| Primary disease: Disease group | Congenital esophageal atresia | 6 | (26.09) |
| Airway stenosis | 5 | (21.74) | |
| Neuromuscular disease | 5 | (21.74) | |
| Inherited metabolic diseasea | 4 | (17.39) | |
| Pulmonary hypoplasia | 3 | (13.04) | |
| Primary disease: Disease name | Congenital esophageal atresia | 6 | (26.09) |
| Propionic acidemia | 2 | (8.70) | |
| Pharyngeal stenosis | 2 | (8.70) | |
| Laryngomalacia | 2 | (8.70) | |
| Congenital diaphragmatic hernia | 2 | (8.70) | |
| Duchenne muscular dystrophy | 1 | (4.35) | |
| Pharyngeal stenosis/laryngomalacia | 1 | (4.35) | |
| Very long-chain acyl-coenzyme A dehydrogenase deficiency | 1 | (4.35) | |
| Myotonic dystrophy | 1 | (4.35) | |
| Spinal muscular atrophy | 1 | (4.35) | |
| Congenital myopathy | 1 | (4.35) | |
| Congenital myopathy (suspected Bethlem myopathy) | 1 | (4.35) | |
| Congenital cystic lung disease | 1 | (4.35) | |
| Medium-chain acyl-coenzyme A dehydrogenase deficiency | 1 | (4.35) | |
a
Propionic acidemia (2 cases), medium-chain acyl-CoA dehydrogenase (1 case), deficiency very-long-chain acyl-CoA dehydrogenase (1 case).