. Author manuscript; available in PMC: 2023 Aug 7.

Published in final edited form as: Am J Med Genet A. 2023 Mar 15;191(5):1339–1349. doi: 10.1002/ajmg.a.63181

TABLE 5.

Survival probabilities and 95% confidence intervals for individuals with Turner syndrome.

Survival time	Number at risk		Number of deaths		Overall survival probability
Survival time	All cases	Cases without HLH^a	All cases	Cases without HLH	All cases	Cases without HLH
1 day	745	702	13	13	98.4 (97.2–99.1)	98.2 (96.9–98.9)
7 days	731	693	23	17	97.0 (95.6–98.0)	97.6 (96.2–98.5)
28 days	719	687	33	22	95.6 (94.0–96.9)	96.9 (95.3–97.9)
1 year^b	593	581	64	37	91.8 (89.6–93.5)	94.8 (92.8–96.2)
2 years	568	558	66	37	91.4 (89.3–93.2)	94.8 (92.8–96.2)
5 years^c	485	478	68	38	91.1 (88.9–92.9)	94.6 (92.6–96.0)

HLH = hypoplastic left heart.

All programs except South Carolina provided data to assess survival up to and including one year.

Arkansas, Utah, Texas, and Metropolitan Atlanta Congenital Defects Program (MACDP) provided data to assess 2- and 5-year overall survival.