Table 1.

American College of Rheumatology case definitions for neuropsychiatric SLE (1999) [21]

Central nervous system (CNS)
Diffuse	Acute confusional state
	Anxiety disorder
	Aseptic meningitis
	Cognitive dysfunction
	Demyelinating syndrome (Fig. 1A)
	Headache
	Mood disorder
	Psychosis
Focal	Cerebrovascular disease (Fig. 2)
	Movement disorder
	Myelopathy (Fig. 1B)
	Seizures
Peripheral nervous system (PNS)
Acute inflammatory demyelinating polyradiculoneuropathy (Guillain-Barré syndrome) (Fig. 1C)
Autonomic disorder
Cranial neuropathy
Mononeuropathy
Myasthenia gravis
Plexopathy
Polyneuropathy