Figure 6. Disease-associated mutations in the NPT2A internal PDZ ligand block FGF23- or PTH- inhibitable phosphate transport.
Arg495 (R495) in the 494TRL496 motif was substituted by Cys (R495 C) or His (R495 H). CRISPR/Cas9 Npt2a knockout OK cells were transfected with the indicated NPT2A variants. Phosphate uptake was assayed in the presence or absence of FGF23 or PTH, as indicated. n = 12, **** P < 0.0001 PTH or FGF23 vs. control.