Table 5.

Changes in food frequency (FFQ) at baseline, 3-months and 6-months.

FFQ (Portions per Week) (n = 17) (Median [P25–P75])
Food	Portion Size	Baseline	3-Months Post Sapropterin	6-Months Post Sapropterin	Friedman Test (p Value <0.05)
Cow’s milk	30 mL	0 [0–1.5]	1 [0–66]	1 [0–42]	0.001
Low protein milk	200–250 mL	7 [4.5–14]	3.5 [1–11]	5 [0–7]	0.007
Regular cheese	15–20 g	0 [0–0]	0 [0–3]	0 [0–0]	0.165
Low protein cheese	20 g	3.5 [1–5]	0 [0–3]	0 [0–3]	0.172
Meat/fish/eggs	60–80 g 1 medium egg	0 [0–0.5]	1 [0–6]	0 [0–7]	0.005
Low protein meat/fish/eggs	80 g	0 [0–1.5]	0 [0–0]	0 [0–1]	0.094
Regular bread	30–70 g	0.5 [0–5.5]	7 [4.5–12]	9 [6–14]	0.010
Low protein bread	30–70 g	1.5 [0–6.5]	0 [0–1]	0 [0–2]	0.028
Regular pasta	15 g (cooked)	0 [0–2]	2 [0–5.5]	3 [0–13]	0.011
Low protein pasta	80–100 g (cooked)	2.5 [2–5]	0 [0–2]	0 [0–2]	<0.001
Chips and processed potatoes	30–55 g	9 [3–14]	11.5 [3.5–16]	6 [6–13]	0.678
Vegetables	20–60 g	8 [5–17]	12 [4.5–15.5]	8 [4–19]	0.854
Fruit (fresh)	80–100 g (1 piece)	6 [0.5–14]	3 [0.5–10.5]	7 [3–14]	0.614