TABLE 2.
Histological features in INCPH (PSVD) with description and alternative terminologies4
| Serial number | Specific features | Alternative names | Description |
|---|---|---|---|
| 1 | Obliterative portal venopathy | Phlebosclerosis, PV obliteration, PV stenosis, hepatoportal sclerosis | Incomplete or complete luminal narrowing of PV branches along with PV wall thickening and fibrosis |
| 2 | Nodular regenerative hyperplasia | — | Micronodular changes of hepatic parenchyma without any significant fibrosis |
| 3 | Incomplete septal fibrosis/cirrhosis | — | Fine fibrous septa that arise from a PT and terminate blindly within a hepatic lobule without any definitive bridge to central veins or other PT |
| Nonspecific features | Alternative names | Description | |
| 1. PT abnormalities | Herniated PV | Aberrant vessels, shunt vessels | A PV branch originating from PT abutting the adjacent hepatic parenchyma without a rim of intervening connective tissue |
| Periportal abnormal vessels | Aberrant vessels, cavernous transformation, periportal shunting vessels | Single or multiple thin-walled vascular channels of variable caliber in close contact with the PT but not within | |
| Hyper-vascularized PT | Multiplicity of PVs, PT angiomatosis, angiomatoid lesion, angiomatous transformation of PT | Increased number of PV branches within PT | |
| 2 | Architectural disturbance | — | Irregular distribution of PTs and central veins |
| 3 | Nonzonal sinusoidal dilatation | — | Sinusoidal lumen (nonzonal) wider than a single liver cell plate |
| 4 | Mild perisinusoidal fibrosis | — | Fibrosis around the sinusoids |
Abbreviations: INCPH, idiopathic noncirrhotic portal hypertension; PSVD, portosinusoidal vascular disorder; PT, portal tract; PV, portal vein.