Table 3.
Comparison Between Patients With and Without RV Systolic Dysfunction
| Parameters | Normal RV function | RV dysfunction | P value |
|---|---|---|---|
| (n=44) | (n=46) | ||
| Age, y | 27 (22 to 32.5) | 28.5 (23 to 35) | 0.83 |
| Body mass index, kg/m2 | 16.8 (14.8 to 21) | 17.5 (14.4 to 22.9) | 0.65 |
| Body surface area, m2 | 1.4 (1.3 to 1.6) | 1.4 (1.2 to 1.7) | 0.92 |
| Wheelchair bounded | 44 (100) | 45 (97.8) | 0.99 |
| Systolic blood pressure, mm Hg | 108 (99 to 118) | 106 (96 to 116) | 0.3 |
| Diastolic blood pressure, mm Hg | 65 (59 to 75) | 60 (59 to 75) | 0.99 |
| Heart rate, bpm | 87 (76 to 100) | 82 (70 to 94) | 0.37 |
| Angiotensin‐converting enzyme inhibitors | 41 (93.2) | 43 (93.5) | 0.99 |
| Beta blockers | 23 (52.3) | 33 (71.7) | 0.08 |
| Mineraloreceptor antagonists | 2 (4.5) | 4 (8.7) | 0.68 |
| Loop diuretics | 1 (2.3) | 3 (6.5) | 0.62 |
| Steroids | 2 (4.5) | 6 (13) | 0.27 |
| Left bundle branch block | 2 (4.9) | 1 (2.4) | 0.99 |
| Pulmonary forced vital capacity, % | 11 (6 to 20) | 9.5 (5 to 14) | 0.61 |
| Home mechanical ventilation 24 h/24 h | 24 (54.5) | 27 (60) | 0.67 |
| Tracheostomy | 18 (40.9) | 18 (39.1) | 0.99 |
| Diurnal Pco 2, mm Hg | 37.5 (29.5 to 43.5) | 42 (35.5 to 45.5) | 0.24 |
| pH | 7.42 (7.4 to 7.5) | 7.39 (7.4 to 7.4) | 0.13 |
| Excess basis, mmol/L | 0.35 (−2.3 to 2.5) | −0.5 (−2.2 to 2.2) | 0.66 |
| ALT, μ/L | 36.5 (26 to 45) | 42 (28 to 48) | 0.52 |
| AST, μ/L | 28 (23 to 33) | 30.5 (24 to 34.5) | 0.3 |
| GGT, μ/L | 25 (15 to 49) | 35 (20 to 48) | 0.79 |
| ALP, μ/L | 90 (64 to 115) | 85 (65 to 105.5) | 0.89 |
| Creatinine, μmol/L | 12.5 (7 to 20) | 14 (8 to 20) | 0.9 |
| Hemoglobin, g/dL | 13.25 (12.6 to 14.2) | 13.75 (13.1 to 14.5) | 0.29 |
| Lymphocytes/mm3 | 1780 (1190 to 2040) | 1845 (1405 to 2135) | 0.85 |
| Albuminemia, g/L | 39 (37 to 42) | 40 (37 to 42) | 0.99 |
| Total bilirubin, μmol/L | 8 (7 to 13) | 8 (6 to 14) | 0.82 |
Data expressed as median (IQR) or N (%). ALP indicates alkaline phosphatase; ALT, alanine transaminase; AST, aspartate transaminase; GGT, gamma‐glutamyl transpeptidase; and RV, right ventricular.