| Mitochondria: | BCAA + 2-OG → BCKA + Glu |
| Glu + OA → 2-OG + L-Asp | |
| AGC1: | L-Asp transport to the cytosol |
| Cytosol: | L-Asp + IMP + GTP → adenylosuccinate + GDP + Pi |
| adenylosuccinate → fumarate + AMP | |
| AMP + H2O → IMP + NH3 | |
| or | |
| AMP + ATP → ADP + ADP | |
| ADP + creatine phosphate → ATP + creatine |