Table 2.
Baseline characteristics of participants
Authors | No. of participants | Age (yr) | Gender (% of female) | Height (m) | Leg length (m) | HTT CAG repeat number | TMS | TFC | Control matching |
---|---|---|---|---|---|---|---|---|---|
Andrzejewski et al. [43] | HD: 15 | 56.8 ± 6.6 | 40 | - | - | - | 42.3 ± 13.3 | - | Not stated |
CO: 5 | 53.4 ± 20.4 | 60 | |||||||
Anwar et al. [26] | HD: 16 | 53.31 ± 7.1 | 25 | 1.7 ± 0.08 | 1.02 ± 0.05 | 43.44 ± 1.79 | - | - | Age, height, weight, leg length |
CO: 16 | 53.5 ± 6.54 | 25 | 1.7 ± 0.07 | 1.01 ± 0.04 | |||||
Beckmann et al. [1] | Pre: 26 | 37.9 ± 11.1 | 53.85 | - | - | 41.6 ± 2.3 | 1 ± 1.4 | 12.96 ± 0.2 | Age |
HD: 40 | 47.7 ± 9.9 | 60 | 44.1 ± 2.9 | 33.6 ± 16.7 | 8.9 ± 3.5 | ||||
CO: 30 | 38.6‡ | 63.33 | |||||||
Bilney et al. [29] | HD: 30 | 51.2 ± 10.6 | 30 | 1.73 ± 0.11 | - | 43.3 ± 2.57 | 40.92 ± 26.32 | - | Age, gender, height |
CO: 30 | 50.9 ± 11.6 | 30 | 1.74 ± 0.9 | ||||||
Churchyard et al. [32] | HD: 20 | 58.2 ± 12.9 | 20 | - | - | - | 44.1 ± 25.5 | - | Age, height |
CO: 16 | 55.4 ± 10.5 | 18.75 | |||||||
Collett et al. [2] | Pre: 7 | 48 ± 16 | 71.4 | 1.69 ± 0.11 | 0.93 ± 0.07 | 41 ± 3 | 1 (0–4) | 13 (13–13) | Age, gender, BMI, height, leg length |
HD I: 16 | 47 ± 10 | 50 | 1.69 ± 0.10 | 0.92 ± 0.06 | 45 ± 3 | 28.5 (11–73) | 9 (7–13) | ||
HD II: 12 | 50 ± 14 | 25 | 1.69 ± 0.07 | 0.9 ± 0.03 | 47 ± 7 | 59.5 (17–78)* | 5 (4–6)* | ||
CO: 22 | 46 ± 10 | 50 | 1.7 ± 0.1 | 0.91 ± 0.06 | |||||
Dalton et al. [21] | Pre: 7 | 44.8 ± 11.7 | 60 | 1.71 ± 0.1 | 0.92 ± 0.06 | - | 4.8 ± 5.3 | 13 | Age, gender, weight, height, leg length |
HD: 14 | 51.83 ± 14.8 | 43 | 1.68 ± 0.09 | 0.9 ± 0.04 | 54.15 ± 13.02 | 6.33 ± 2.18 | |||
CO: 22 | 56.4 ± 10.9 | 50 | 1.71 ± 0.07 | 0.93 ± 0.05 | |||||
Danoudis and Iansek [44] | HD: 17 | 60 ± 10.5 | 47 | 1.71 ± 0.07 | 0.873 ± 0.047 | 40–51† | 25.8 ± 10.63 | 2 | Not stated |
CO: 21 | 71.7 ± 4 | 62 | 1.66 ± 0.06 | 0.86 ± 0.04 | |||||
de Tommaso et al. [45] | HD: 24 | 48.13 ± 11.53 | 50 | - | - | 44.33 ± 0 | 37.71 ± 20.21 | - | Age, gender |
CO: 14 | 48.8 ± 14.13 | 50 | |||||||
Delval et al. [28] | HD: 15 | 47 ± 11.2 | 53 | 1.68 ± 0.1 | - | 43.6 ± 3.3 | 28.7 ± 22 | 10.9 ± 1.6 | Age, gender |
CO: 15 | 47.9 ± 11.2 | NS | 1.7 ± 0.1 | ||||||
Delval et al. [30] | HD: 15 | 43.9 ± 9.8 | 52 | 1.69 ± 0.1 | - | 47 ± 4 | 42 ± 17.1 | 9 ± 2.5 | Gender, age, height |
CO: 15 | 40.5 ± 10.5 | NS | 1.72 ± 0.09 | ||||||
Delval et al. [22] | Pre: 17 | 36.5 (29–42) | 50.88 | 1.73 (1.69–1.78) | 0.91 (0.89–0.93) | - | 3 (2–6.25)* | 13 | Age |
CO: 57 | 38 (29–61)* | 47.37 | 1.73 (1.64–1.77)* | 0.9 (0.87–0.93)* | |||||
Desai et al. [46] | HD: 33 | 54.7 ± 12.6 | 39.4 | - | - | - | 39 ± 15 | 11 ± 2 | Age, gender |
CO: 15 | 53.2 ± 13.2 | 46.67 | |||||||
Gaßner et al. [9] | HD: 43 | 50 ± 11.1 | 41.86 | 1.739 ± 0.09 | - | 44.1 ± 4.2 | 38.2 ± 17.9 | 9.1 ± 3.4 | Age, gender, weight, height |
CO: 43 | 51 ± 11.3 | 51.12 | 1.737 ± 0.095 | ||||||
Grimbergen et al. [3] | HD: 45 | 59.1 ± 10.1 | 51.1 | - | - | - | 32.93 | 9.8 | Age |
CO: 27 | 52.2 ± 8.5 | 60 | |||||||
Hausdorff et al. [11] | HD: 17 | 46.3 ± 12.8 | 64.7 | 1.85 ± 0.09 | - | - | - | 7.4 ± 3.6 | Gender, weight, height |
CO: 10 | 34.5 ± 13.4 | 90 | 1.83 ± 0.09 | ||||||
Hausdorff et al. [10] | HD: 20 | 47 (29–71) | 70 | 1.83 ± 0.02 | - | - | - | > 9, n = 6 | Age, weight, height |
CO: 16 | 39 (20–74) | 87.5 | 1.83 ± 0.02 | 5–9, n = 7 | |||||
< 5, n = 8 | |||||||||
Koller and Trimble [24] | HD: 13 | 55.6‡ | 0 | 1.83 ± 0.02 | - | - | - | - | Not stated |
CO: 10 | 52.2‡ | NS | 1.83 ± 0.02 | ||||||
Muratori et al. [47] | HD: 43 | 53.6 ± 11.6 | 41.86 | - | - | - | 40.6 ± 16.4 | 10.6 ± 2.2 | Gender, age |
CO: 15 | 52.2 ± 13.2 | 46.67 | |||||||
Purcell et al. [31] | HD: 17 | 55 ± 9.66 | 41.18 | - | - | - | 21.86 ± 9.86 | - | Not stated |
CO: 17 | 56.47 ± 9.3 | 47.06 | |||||||
Pyo et al. [25] | HD: 7 | 59.14 ± 12.94 | 57.1 | - | - | 43.14 ± 8.20 | 27.86 ± 8.44 | 5.14 ± 1.96 | Age, gender, weight, height |
CO: 7 | 55.71 ± 14.58 | NS | |||||||
Radovanović et al. [27] | HD: 16 | 51.38 ± 9.65 | 50 | - | - | - | - | - | Age, gender |
CO: 26 | 51.96 ± 8.53 | 50 | |||||||
Rao et al. [8] | HD: 12 | 50 ± 7.8 | 41.67 | - | - | - | - | 8 ± 4.15 | Age |
CO: 22 | 41.67 | ||||||||
Rao et al. [14] | Pre: 15 | 36.92 ± 2.05 | 60 | - | - | 42.84 ± 0.57 | 2.78 ± 1.62 | 13 ± 0 | Age |
HD: 30 | 48.81 ± 10.22 (HD I) | 40 | 44.25 ± 4.16 | 29.64 ± 11.55 | 11.72 ± 0.78 | ||||
53.25 ± 11.21 (HD II) | 50 | 45 ± 0 | 46.33 ± 13.5 | 8.83 ± 1.11 | |||||
47.25 ± 8.12 (HD III) | 60 | 46 ± 3.05 | 56.13 ± 15.72 | 5 ± 0.96 | |||||
CO: 20 | 44.3 ± 9.05 | 60 | |||||||
Reynolds et al. [23] | HD: 6 | 33–61† | 50 | - | - | - | - | - | Age |
CO: 30 | NS |
Data presented as mean ± standard deviation, unless otherwise stated.
data presented as median and range;
data presented as range only;
data presented as mean only.
TMS, total motor score; TFC, total functional capacity; Pre, premanifest participants; HD, Huntington’s disease; CO, controls; NS, not stated; BMI, body mass index.