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. 2023 Sep 15;12(10):631–650. doi: 10.1093/stcltm/szad051

Table 7.

Demographic characteristics and anatomical follow-up parameters of Group 4 (natural course).

Patient No Genetic mutation Eye Horizontal EZW Vertical EZW FAF field
Time0 Time1 Time0 Time1 Time0 Time1
1 RHO R 3.74 3.06 3.41 1.91 8.6 5.1
L 3.46 2.71 3.61 2.74 8.9 5.4
2 PCARE R 8.30 5.81 7.77 5.43 46.4 29.8
L 8.30 5.81 7.97 5.57 46.8 30.1
3 RPGR R 2.12 0.81 2.76 1.37 4.7 0.9
L 2.71 1.32 3.01 1.56 1.9 1.3
4 USH2A R 7.45 6.33 5.68 4.81 62.9 53.8
L 8.24 6.96 7.98 6.81 71.8 61.5
5 PDE6B R 3.73 2.35 2.87 2.01 9.1 6.2
L 3.79 2.37 3.68 2.76 14.8 8.9
6 BBS2 R 1.92 1.12 1.82 1.03 3.8 1.4
L 1.60 1.14 1.55 0.86 2.2 0.81
7 PDE6B R 3.11 2.06 3.50 2.74 10.1 6.2
L 3.02 2.01 3.41 2.54 9.8 4.6
8 RHO R 5.75 4.82 5.01 4.24 26.1 16.6
L 5.69 4.78 5.22 4.37 25.9 16.5
9 RP1 R 2.40 1.98 2.40 2.00 4.2 3.7
L 2.70 2.14 2.60 2.06 4.8 4.0
10 USH2A R 5.08 4.24 4.98 4.16 22.6 16.9
L 4.98 4.19 4.71 4.14 17.2 16.6
11 BBS6 R 1.34 0.91 1.38 1.02 1.4 1.1
L 1.29 0.87 1.30 0.90 1.2 0.84
12 TULP1 R 1.77 1.24 1.53 1.10 3.9 3.1
L 1.54 1.12 1.70 1.25 3.2 2.9
13 RHO R 2.86 2.41 2.77 2.38 5.6 5.0
L 2.76 2.34 2.65 2.32 5.1 4.6
14 RHO R 2.33 2.02 2.00 1.74 4.1 3.9
L 1.97 1.71 1.89 1.69 3.7 3.1
15 EYS R 1.88 1.42 1.88 1.43 3.6 2.2
L 2.05 1.78 2.49 2.32 5.7 4.6
16 ABCA4 R 2.53 1.81 2.48 1.78 6.1 5.2
L 2.50 1.79 2.48 1.78 6.0 5.1

Time0 (baseline): initial examination.

Time1: 36th month examination.

Abbreviations: EZW, ellipsoid zone width (mm); FAF, fundus autofluorescence (mm2).