Figure 3-2.

Glycolytic pathways. Glycogen storage diseases (GSDs) are designated with Roman numerals. GSD I and VI are not included since they do not cause muscle disease. The numerals denote defects in the following enzymes: II, acid maltase; III, debrancher; IV, brancher; V, myophosphorylase; VII, phosphofructokinase; VIII, phosphorylase b kinase; IX, phosphoglycerate kinase; X, phosphoglycerate mutase; XI, lactate dehydrogenase; XII, aldolase A; XIII, beta enolase, XIV, phosphoglucomutase 1. cAMP = cyclic adenosine monophosphate; UDPG = uridine diphosphoglucose; PLD = phosphorylase-limit dextrin; TPI = triose phosphate isomerase.