Figure 2-20.
Muscle biopsy immunostained for A, α-sarcoglycan; B, β-sarcoglycan; C, γ-sarcoglycan; and D, δ-sarcoglycan demonstrating diminished staining for all four in a woman with limb-girdle muscular dystrophy type 2D, α-sarcoglycanopathy. Courtesy of Charles S. Specht, MD.